A case of bilateral diffuse villous hyperplasia of the choroid plexus： Literature review of surgical treatment for bilateral diffuse villous hyperplasia of the choroid plexus and choroid plexus papilloma

Diffuse villous hyperplasia of the choroid plexus（DVHCP）and choroid plexus papilloma（CPP）are rare benign choroid plexus tumors that are usually diagnosed as a result of progressive hydrocephalus, especially in childhood. Here, we present the case of a boy who was diagnosed with progressive hydro-cephalus before birth. He was born by caesarean section at 38 weeks, because of progressive hydrocepha-lus. We performed a cisterna magna‒peritoneal shunt procedure at 1 month after birth. Postoperatively, cerebrospinal fluid（CSF）leak under the scalp, progressive ascites and hydrocele testis were observed, which were considered a result of CSF overproduction. Endoscopic coagulation of the right choroid plexus was carried out, and DVHCP was diagnosed pathologically and clinically. Following an initial improvement in the CSF leak under the scalp, the ascites, and hydrocele testis, all recurred two months after micro-scopic surgery. An endoscopic plexectomy of the left choroid plexus was performed at the age of 11 months with subsequent CSF control. There are few case reports of bilateral DVHCP and CPP in the liter-ature. Herein, we provide a detailed clinical course of our case and previous cases focusing on surgical pro-cedures.