Human herpes virus-8-negative primary effusion lymphoma in a patient with common variable immunodeficiency

Akiko Hisamoto, Hiromichi Yamane, Akio Hiraki, Yoshinobu Maeda, Nobuharu Fujii, Kenji Sasaki, Toshitugu Miyake, Takashi Sasaki, Tohru Nakamura, Katsuyuki Kiura, Mitsune Tanimoto, Haruhito Kamei

Research output: Contribution to journalArticlepeer-review

27 Citations (Scopus)

Abstract

Primary effusion lymphoma (PEL) is a newly described high-grade B cell lymphoma developing in association with human herpes virus type 8 (HHV-8) in human immunodeficiency virus (HIV)-infecting individuals. Common variable immunodeficiency (CVID) is a primary immunodeficiency disease characterized by reduced serum immunoglobulin and heterogeneous clinical features. The risk of cancer in CVID patients is increased. Here, we describe a PEL that developed in the pleural and pericardial cavities of an HIV-negative and HHV-8-negative patient with CVID.

Original languageEnglish
Pages (from-to)2019-2022
Number of pages4
JournalLeukemia and Lymphoma
Volume44
Issue number11
DOIs
Publication statusPublished - Nov 2003

Keywords

  • Common variable immunodeficiency
  • Human herpes virus 8
  • Non-Hodgkin's lymphoma
  • Primary effusion lymphoma

ASJC Scopus subject areas

  • Hematology
  • Oncology
  • Cancer Research

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